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WOUNDS IN CHILDREN AND EPIDERMOLYSIS BULLOSA

NIVES PUSTIŠEK ; Klinički bolnički centar “Sestre milosrdnice”, Klinika za pedijatriju, Zagreb, Hrvatska
IRENA BABIĆ ; Klinički bolnički centar “Sestre milosrdnice”, Klinika za dječju kirurgiju, Zagreb, Hrvatska
ANTUN KLJENAK ; Klinički bolnički centar “Sestre milosrdnice”, Klinika za dječju kirurgiju, Zagreb, Hrvatska
NEDA STRIBER ; Klinički bolnički centar “Sestre milosrdnice”, Klinika za dječju kirurgiju, Zagreb, Hrvatska
STJEPAN VIŠNJIĆ ; Klinički bolnički centar “Sestre milosrdnice”, Klinika za dječju kirurgiju, Zagreb, Hrvatska
MAJA KARAMAN ILIĆ ; Klinički bolnički centar Zagreb, Zagreb, Hrvatska


Puni tekst: hrvatski pdf 57 Kb

str. 119-122

preuzimanja: 2.020

citiraj


Sažetak

Epidermolysis bullosa is a group of inherited disorders characterized by blister formation on the skin and mucous membrane as the result of molecular defects in genes coding for different structural proteins. They present with a wide clinical spectrum of manifestations because of a variety of molecular defects. Therapy depends on the form of the disease, severity and extent of skin involvement and extracutaneous manifestations, and consists of supportive skin care and supportive care for other organ systems. Skin care includes protection against trauma, proper skin care, treatment of blisters and erosions, and regular dermatological controls for early detection of skin cancer.

Ključne riječi

epidermolysis bullosa; skin care; treatment

Hrčak ID:

98731

URI

https://hrcak.srce.hr/98731

Datum izdavanja:

25.2.2013.

Podaci na drugim jezicima: hrvatski

Posjeta: 3.005 *