Paediatria Croatica, Vol. 51 No. 1, 2007.
Recenzija, Prikaz slučaja
EWING SARCOMA OF THE RIB – CASE REPORT
MIRKO ŽGANJER
IRENEJ CIGIT
ANTE ČIZMIĆ
ALEKSANDRA BONEVSKI
JASMINKA STEPAN
GORDANA JAKOVLJEVIĆ
IGOR BUMČI
ANTUN KLJENAK
Sažetak
Ewing sarcoma, a highly malignant primary bone tumor, was first described by James Ewing in 1921 (1). Ewing sarcoma usually presents in childhood or early adulthood, with its peak between 10 and 20 years of age, although it can occur in younger children and older adults. The most common areas in which it occurs are the pelvis, the femur, the humerus and the ribs. Ewing sarcoma is the second most common malignant bone tumor in young patients and it is the most lethal bone tumor. Tumor occurrence ranges from 0.3 cases per 1 000 000 children younger than 3 years to as high as 4.6 cases per 1 000 000 adolescents aged 15-19 years. The annual incidence rate averages less than 2 cases per 1 000 000 children. The male-to-female ratio is 1.5:1 (2-6). Survival rate is 60-70% with low-risk, in a localized tumor, intermediate risk (30%) when the tumor has spread to lungs and advanced risk (less than 10%) when the tumor has spread further to bone, bone marrow and/or other tissue (7, 8). We present an 8 year-old girl with Ewing sarcoma of the rib.
Ključne riječi
Descriptors: SARCOMA, EWING' S – diagnosis, therapy; BONE NEOPLASMS – diagnosis, therapy; RIBS
Hrčak ID:
11856
URI
Datum izdavanja:
2.5.2007.
Posjeta: 7.566 *