Paediatria Croatica, Vol. 61 No. 3, 2017.
Pregledni rad
https://doi.org/10.13112/PC.2017.20
Dental management in osteogenesis imperfecta
Hrvoje Brkić
orcid.org/0000-0003-4284-7739
Ivana Savić Pavičin
orcid.org/0000-0002-5210-1765
; Stomatološki fakultet
Sažetak
Osteogenesis imperfecta is a very rare heterogeneous genetic disorder associated with the development of connective tissue resulting
in fragile bones and frequent fractures. More than 50% of patients aff ected with osteogenesis imperfecta have a hereditary developmental
disorder known as dentinogenesis imperfecta. Dentinogenesis imperfecta is caused by irregularities in the formation,
composition and organization of dentin matrix during tooth development. It is caused by mutations of the genes that encode basic
proteins of the organic matrix, collagens and phosphoproteins. The purpose of this review is to describe the histopathologic and
clinical features of teeth typical of dentinogenesis imperfecta type I, which occurs within osteogenesis imperfecta, with special
emphasis on targeted dental treatment to achieve optimal rehabilitation of the masticatory system.
Ključne riječi
developmental bone disease; dentinogenesis imperfecta; rehabilitation
Hrčak ID:
201169
URI
Datum izdavanja:
25.9.2017.
Posjeta: 1.345 *