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WOUNDS IN CHILDREN AND EPIDERMOLYSIS BULLOSA
NIVES PUSTIŠEK
; „Sestre milosrdnice“ University Hospital Center, University Department of Pediatrics, Zagreb, Croatia
IRENA BABIĆ
; „Sestre milosrdnice“ University Hospital Center, Department of Pediatric Surgery, Zagreb, Croatia
ANTUN KLJENAK
; „Sestre milosrdnice“ University Hospital Center, Department of Pediatric Surgery, Zagreb, Croatia
NEDA STRIBER
; „Sestre milosrdnice“ University Hospital Center, Department of Pediatric Surgery, Zagreb, Croatia
STJEPAN VIŠNJIĆ
; „Sestre milosrdnice“ University Hospital Center, Department of Pediatric Surgery, Zagreb, Croatia
MAJA KARAMAN ILIĆ
; Zagreb University Hospital Center, Zagreb, Croatia
Abstract
Epidermolysis bullosa is a group of inherited disorders characterized by blister formation on the skin and mucous membrane as the result of molecular defects in genes coding for different structural proteins. They present with a wide clinical spectrum of manifestations because of a variety of molecular defects. Therapy depends on the form of the disease, severity and extent of skin involvement and extracutaneous manifestations, and consists of supportive skin care and supportive care for other organ systems. Skin care includes protection against trauma, proper skin care, treatment of blisters and erosions, and regular dermatological controls for early detection of skin cancer.
Keywords
epidermolysis bullosa; skin care; treatment
Hrčak ID:
98731
URI
Publication date:
25.2.2013.
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