Case report, case study

https://doi.org/10.21860/medflum2025_330056

Fibrous Dysplasia – A Rare Occurence in the Temporal Bone: A Case Report

Ema Ahel Ledić orcid.org/0009-0009-4404-0454 ; Klinički bolnički centar Rijeka, Klinika za otorinolaringologiju i kirurgiju glave i vrata, Rijeka, Hrvatska; Sveučilište u Rijeci, Medicinski fakultet, Rijeka, Hrvatska *
Anamaria Baričević ; Sveučilište u Rijeci, Medicinski fakultet, Rijeka, Hrvatska
Darko Ledić ; Sveučilište u Rijeci, Medicinski fakultet, Rijeka, Hrvatska; Klinički bolnički centar Rijeka, Klinika za neurokirurgiju, Rijeka, Hrvatska
Marko Velepič orcid.org/0000-0002-9826-798X ; Klinički bolnički centar Rijeka, Klinika za otorinolaringologiju i kirurgiju glave i vrata, Rijeka, Hrvatska; Sveučilište u Rijeci, Medicinski fakultet, Rijeka, Hrvatska

* Corresponding author.

Abstract

Aim: Fibrous dysplasia is a rare and benign disorder, in which normal bone elements are replaced by fibrous tissue. Temporal bone involvement and adult onset of disease is least frequently reported. Case Report: A case of fibrous dysplasia of temporal bone in a 61-year-old female which presented with a headache, tinnitus and hearing loss is reported. Sensorineural hearing loss was the initial finding on the audiogram. Computed tomography showed an expansive, strictly limited sclerotic lesion of the dorsal part of the pyramid of the left temporal bone spreading into the mastoid cells. Magnetic resonance of the temporal bone and inner ear showed two expansive formations – one in the clivus and the other in the pyramid of the left temporal bone. Both CT and MRI pointed to fibrous dysplasia, but definite histopathological finding was required to exclude malignancy. Mastoidectomy with a reduction of lesion was performed. Histopathological examination revealed sclerotic bone with irregular bony trabeculae – fibrous dysplasia. Whole body low-dose computed tomography was performed and no other occurrences of fibrous dysplasia were detected. For the clival lesion neurosurgeon decided for the „wait and watch policy“ as the patient was asymptomatic after the surgery. Patient is under regular follow-up for both otorhinolaryngologist and neurosurgeon with good functional results, without subjective complaints of headaches, while hearing remained stationary. Conclusion: This case highlights the importance of surgery as a confirmation for diagnosis and regular follow-up in selective cases of temporal bone fibrous dysplasia.

Keywords

fibrous dysplasia of bone; mastoidectomy; temporal bone

Hrčak ID:

330056

URI

https://hrcak.srce.hr/330056

Publication date:

1.6.2025.

Article data in other languages: croatian

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