Prethodno priopćenje
Peutz-Jeghers Syndrome Complicated with Intussusception: Enteroscopic Polyps Resections through Laparotomy
Zdravko Perko
; University of Split, Split University Hospital Center, Department of Surgery, Split, Croatia
Dragan Krnic
; University of Split, Split University Hospital Center, Department of Surgery, Split, Croatia
Zenon Pogorelic
; University of Split, Split University Hospital Center, Department of Paediatric Surgery, Split, Croatia
Nikica Druzijanic
; University of Split, Split University Hospital Center, Department of Surgery, Split, Croatia
Miroslav Simunic
; University of Split, Split University Hospital Center, Department of Internal Medicine, Split, Croatia
Kanito Bilan
; University of Split, Split University Hospital Center, Department of Surgery, Split, Croatia
Damir Kraljevic
; University of Split, Split University Hospital Center, Department of Surgery, Split, Croatia
Marina Maras Simunic
; University of Split, Split University Hospital Center, Department of Radiology, Split, Croatia
Sažetak
Peutz-Jeghers syndrome is an autosomal dominant inherited disorder characterized by intestinal hamartomatous polyps in association with mucocutaneous pigmentations. Here we present a case of a 30-year-old woman who was hospitalized and underwent diagnostic procedures because of crampy adbdominal pain. Physical examination on admission revealed pigmented spots around lips and on the oral mucosa. Multiple polyps were found in stomach, small and large intestine, with signs of initial ileo-ileal intussusception. After endoscopic removal of achievable polyps, we applied gastroscope through laparotomy and enterotomy and removed total number of 34 polyps from small bowell. The polyps were found to be mostly hamartomatous at histological examination. This procedure can provide removal of the most polyps, which are potentially premalignant, also with less complicationes than after multiple intestinal resectiones.
Ključne riječi
Peutz-Jeghers syndrome; endoscopic polypectomy; intussusception
Hrčak ID:
99609
URI
Datum izdavanja:
3.4.2013.
Posjeta: 978 *