Pregledni rad

https://doi.org/10.57140/mj.53.2.4

Herlyn-Werner-Wunderlich syndrome with pyohematocolpos: a case report and review of literature

Damir Zudenigo ; Clinical hospital "Sveti Duh", Department of obstetrics and gynecology
Ingrid Marton ; Clinical hospital "Sveti Duh", Department of obstetrics and gynecology
Petar Lozo ; Zadar Health Centre
Dubravko Habek ; Clinical hospital Merkur, Department of obstetrics and gynecology

Sažetak

Herlyn-Werner-Wunderlich syndrome (HWWS) is a rare malformation syndrome of the women
reproductive tract characterized by uterus didelphys with obstructed hemivagina and ipsilateral renal
agenesis. We report here a case of a 20 year-old patient presented to the emergency department with pain
in the right lower quadrant. The clinical exam showed a vaginal fluctuant painful mass obliterating the right
part of the vagina. Transvaginal ultrasound showed uterus didelphys, the right uterus was dilated with a
dense fluid collection which corresponded to pyohematometra. It also revealed a dense vaginal collection
which corresponded to pyohematocolpos. Abdominal ultrasound showed the absence of a right kidney.
The laparoscopy showed uterus didelphys with a large right uterus. We performed the resection of the
vaginal septum to reconstruct one vagina. The first follow-up visit revealed a healthy wound with no
adhesion of the vaginal wall. Prompt and accurate diagnosis of female reproductive tract disorders,
including HWWS, is necessary to prevent complications and preserve future fertility.

Ključne riječi

Herlyn-Werner-Wunderlich syndrome; pyohematocolpos; pyohematometra; ultrasound; laparoscopy

Hrčak ID:

307329

URI

https://hrcak.srce.hr/307329

Datum izdavanja:

21.8.2023.

Posjeta: 251 *