Liječnički vjesnik, Vol. 146 No. 1-2, 2024.
Stručni rad
https://doi.org/10.26800/LV-146-1-2-5
Mimics of hereditary angioedema
Marko Barešić
; Zavod za kliničku imunologiju i reumatologiju, Klinika za unutarnje bolesti Medicinskog fakulteta Sveučilišta u Zagrebu, Klinički bolnički centar Zagreb
Boris Karanović
orcid.org/0000-0002-5884-1190
; Zavod za kliničku imunologiju i reumatologiju, Klinika za unutarnje bolesti Medicinskog fakulteta Sveučilišta u Zagrebu, Klinički bolnički centar Zagreb
Ljiljana Smiljanić Tomičević
; Zavod za kliničku imunologiju i reumatologiju, Klinika za unutarnje bolesti Medicinskog fakulteta Sveučilišta u Zagrebu, Klinički bolnički centar Zagreb
Branimir Anić
; Zavod za kliničku imunologiju i reumatologiju, Klinika za unutarnje bolesti Medicinskog fakulteta Sveučilišta u Zagrebu, Klinički bolnički centar Zagreb
Sažetak
Hereditary angioedema is a disease characterized by periodic, unpredictable soft tissue swellings of different localization and intensity, is usually self-limiting and in most cases mediated by bradykinin. The disease can cause only a mild esthetic or functional disorder, but can also lead to death in case of upper respiratory tract affection and asphyxia. There are several states that resemble hereditary angioedema, that can be mediated by different molecules (bradykinin, histamine) or different pathophysiological mechanisms. The aim of the article is to address the most frequent mimics of hereditary angioedema that might be encountered in different medical specialties, especially in the emergency department, through illustrative examples from clinical practice.
Ključne riječi
ANGIOEDEMAS, HEREDITARY – diagnosis, etiology, drug therapy; ANDGIOEDEMA – etiology, drug therapy, immunology; COMPLEMENT C1 INHIBITOR PROTEIN – genetics, therapeutic use; BRADYKININ – metabolism; ANGIOTENSIN-CONVERTING ENZYME INHIBITORS – adverse effects; IMMUNOGLOBULIN E – immunology
Hrčak ID:
314679
URI
Datum izdavanja:
27.2.2024.
Posjeta: 175 *