Acta clinica Croatica, Vol. 42 No. 3, 2003.
Other
Intrahepatic Cystic Disease with Congenital Fibrosis (Caroli's Complex Disease): A Case Report and Review of the Literature
Demetrio Tamiolakis
Panagiotis Prassopoulos
Athanasia Kotini
Kiriaki Avgidou
Constantine Simopoulos
Nikolas Papadopoulos
Abstract
A female patient affected by Caroli's disease with congenital fibrosis (Caroli's complex), aged 27 years, is described. Caroli's disease had been asymptomatic to the present. It was recognized as an intraoperative finding during the left hepatectomy procedure after an acute abdominal crisis episode. The main reason for this surgery was the incidence of malignant transformation to cholangiocarcinoma of the cells of the cystic walls. The complex Caroli's disease is more common than other forms. The case report is supplemented with literature review and discussion on the etiopathogenetic mechanisms hypothesized.
Keywords
Caroli's disease, etiology; Caroli's disease, diagnosis; Caroli's disease, complications; Hepatectomy; Case reports
Hrčak ID:
14668
URI
Publication date:
1.9.2003.
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