Professional paper
Platypnea-orthodeoxia-like syndrome in a septic newborn with late appearance of right congenital diaphragmatic hernia
Gorazd Mlakar
; University Medical Centre Ljubljana, Department of Paediatric Surgery and Intensive Care, Bohoriceva 20, 1525 Ljubljana, Slovenia
Stefan Grosek
; University Medical Centre Ljubljana, Department of Paediatric Surgery and Intensive Care, Bohoriceva 20, 1525 Ljubljana, Slovenia
Helena Mole
; University Medical Centre Ljubljana, Department of Obstetrics and Gynaecology, Division of Perinatology, Slajmerjeva ulica 3, 1525 Ljubljana, Slovenia
Silvester Kopriva
; University Medical Centre Ljubljana, Department of Paediatric Surgery and Intensive Care, Bohoriceva 20, 1525 Ljubljana, Slovenia
Ziva Zupancic
; University Medical Centre Ljubljana, Department of Radiology, Zaloska 7, 1525 Ljubljana, Slovenia
Janez Primozic
; University Medical Centre Ljubljana, Department of Paediatric Surgery and Intensive Care, Bohoriceva 20, 1525 Ljubljana, Slovenia
Janez Erzen
; University Medical Centre Ljubljana, Department of Thoracic Surgery, Zaloska 7, 1525 Ljubljana, Slovenia
Abstract
Introduction. Cyanosis and dyspnoea with interatrial shunting of blood occurring without change in body position are termed platypnea-orthodeoxia-like syndrome.
Case presentation. We describe a female newborn with sepsis, who developed cyanosis. Two weeks after the initial appearance of cyanosis she presented with a right-sided diaphragmatic hernia, which was not seen on the initial X-rays. The hernia was surgically repaired. Her postoperative course was uneventful.
Conclusions. In our case, interatrial shunting of blood was presumably caused by disturbed intrathoracic pressures. Positive pressure ventilation and sepsis may also contribute to the development of such a syndrome.
Keywords
cyanosis; right-to-left shunt; infant; sepsis; congenital diaphragmatic hernia
Hrčak ID:
67527
URI
Publication date:
1.4.2011.
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