Original scientific paper
https://doi.org/10.3325/cmj.2019.60.301
Successful separation of xypho-omphalopagus conjoined twins with extrauterine twin-twin transfusion syndrome: a case report
Ruža Grizelj
orcid.org/0000-0001-6077-9878
; Department of Pediatrics, University Hospital Center Zagreb, Zagreb, Croatia
Nada Sindičić Dessardo
; Department of Pediatrics, University Hospital Center Zagreb, Zagreb, Croatia
Krešimir Bulić
; University of Zagreb School of Medicine, Zagreb, Croatia
Tomislav Luetić
; University of Zagreb School of Medicine, Zagreb, Croatia
Danko Mikulić
; Department of Surgery, University Hospital Merkur, Zagreb, Croatia
Anko Antabak
; University of Zagreb School of Medicine, Zagreb, Croatia
Ivica Sjekavica
; University of Zagreb School of Medicine, Zagreb, Croatia
Ana Marija Alduk
; Department of Diagnostic and Interventional Radiology, UniversityHospital Center Zagreb, ZagrebCroatia
Sanja Konosić
; Department of Anesthesiology University Hospital Center Zagreb, Zagreb, Croatia
Karolina Režek Tomašić
; Department of Anesthesiology University Hospital Center Zagreb, Zagreb, Croatia
Tomislav Ćaleta
; Department of Pediatrics, University Hospital Center Zagreb, Zagreb, Croatia
Sanja Pleško
; Department of Clinical and Molecular Microbiology, University Hospital Center Zagreb, Zagreb, Croatia
Dalibor Šarić
; Department of Pediatrics, University Hospital Center Zagreb, Zagreb, Croatia
Jurica Vuković
; Department of Pediatrics, University Hospital Center Zagreb, Zagreb, Croatia
Abstract
Conjoined twining is a rare medical phenomenon, with an
overall prevalence of 1.47 per 100 000 births. This report
describes a successful separation of xypho-omphalopagus
conjoined twins complicated by unbalanced blood
shunting through the porto-systemic anastomoses within
the shared liver parenchyma. Significant extrauterine twintwin
transfusion syndrome caused by unbalanced shunting
is an extremely rare, and probably under-recognized,
hemodynamic complication in conjoined twins necessitating
urgent separation. Progressive deterioration with a
poor outcome can be prevented if the condition is recognized
in a timely manner.
Keywords
Hrčak ID:
240095
URI
Publication date:
15.8.2019.
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