Meeting abstract
https://doi.org/10.26800/LV-142-supp5-15
Idiopathic dilatation of pulmonary artery: a case report
Sara Soraja Nasri
; School of Medicine, University of Zagreb, Zagreb, Croatia
Narcisse Nasri
; School of Medicine, University of Zagreb, Zagreb, Croatia
Gordana Pavliša
; School of Medicine, University of Zagreb, Zagreb, Croatia, Department for Respiratory Diseases Jordanovac Zagreb, University Hospital Center Zagreb, Zagreb, Croatia
Abstract
Idiopathic dilatation of pulmonary arteries (IDPA) is an uncommon condition with an abnormality of pulmonary arteries, it is believed to be a benign anomaly. The incidence is 0.6% in patients with congenital heart disease. IDPA was recognised as a clinical entity in 1923 by Wessler and Jaches. Even though this condition is well known for almost a century, not much is known about its etiopathology and pathophysiology. Diagnosis is set by excluding all congenital or acquired heart lessons that can lead to dilatation of pulmonary arteries. A long period of follow-up is of great importance as in some patients the underlying pathology is discovered later in life.
Keywords
benign anomaly; idiopathic dilatation of pulmonary artery; truncus pulmonalis
Hrčak ID:
251658
URI
Publication date:
27.1.2021.
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