Case report
https://doi.org/10.21860/medflum2022_271165
Retroperitoneal localization of Castelman's disease in a pediatric patient: case report
Ema Šlabek
orcid.org/0000-0001-8463-282X
; Sveučilište u Rijeci, Medicinski fakultet, Katedra za pedijatriju, Rijeka, Hrvatska
Harry Nikolić
; Sveučilište u Rijeci, Medicinski fakultet, Katedra za pedijatriju, Rijeka, Hrvatska; Klinički bolnički centar Rijeka, Klinika za dječju kirurgiju, Rijeka, Hrvatska
Ana Bosak Veršić
; Sveučilište u Rijeci, Medicinski fakultet, Katedra za pedijatriju, Rijeka, Hrvatska; Klinički bolnički centar Rijeka, Klinika za dječju kirurgiju, Rijeka, Hrvatska
Abstract
Aim: Castelman's disease is a rare condition characterized by benign lymph node hyperplasia. The aim of this paper is to present Castelman's disease as a possible cause of retroperitoneal mass in the pediatric population. Case report: A fifteen-year-old boy was admitted to the Department of Pediatric Hematooncology for verification of an expansive formation in the area of omental bursa. The formation was detected by ultrasound during diagnostics due to recurrent vomiting. The boy complained of vomiting during ten days before admission, three to four times daily, usually after breakfast. Ultrasound showed a well-limited formation 4 x 3 centimeters in diameter located between the duodenum and pancreas. Computed tomography confirmed localisation of the tumor showing no signs of infiltration of surrounding structures and magnetic resonance imaging reported benign characteristics. Endoscopic ultrasound guided needle biopsy was preformed and a clinical presumption of a hyaline-vascular variant Castelman's disease was made. Surgical extirpation was performed. Complete tumor resection is a standard treatment for unicentric Castelman's disease. The pathological analysis confirmed the diagnosis of unicentric mixed variant Castelman's. Postoperative recovery went smoothly and the boy was discharged home in good general condition.There were no signs of recurrence of the underlying disease at regular check-ups. Conclusion: Although Castelman's disease is rare, especially localized retroperitoneally and in pediatric population, it should be included in the differential diagnosis when considering retroperitoneal tumorous formations.
Keywords
Castleman disease; pediatrics; retroperitoneal neoplasms; vomiting
Hrčak ID:
271165
URI
Publication date:
1.3.2022.
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