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https://doi.org/10.20471/acc.2016.55.01.22

Castleman’s Disease Presenting as a Tumorous Paracardiac Formation

Ivica Vuković ; Clinical Department of Cardiology, Split University Hospital Center, Split, Croatia
Toni Brešković ; Clinical Department of Cardiology, Split University Hospital Center, Split, Croatia
Darko Duplančić ; Clinical Department of Cardiology, Split University Hospital Center, Split, Croatia
Tonči Batinić ; Clinical Department of Diagnostic and Interventional Radiology, Split University Hospital Center, Split, Croatia
Ivana Štula ; Clinical Department of Diagnostic and Interventional Radiology, Split University Hospital Center, Split, Croatia
Cristian Bulat ; Department of Cardiac Surgery, Split University Hospital Center, Split, Croatia
Snježana Tomić ; Clinical Department of Pathology, Split University Hospital Center, Split, Croatia


Puni tekst: engleski pdf 382 Kb

str. 161-166

preuzimanja: 753

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Sažetak

Castleman’s disease (in the literature also known as angiofollicular hyperplasia) is a rare benign lymphoproliferative disease. Clinically, it can manifest as unicentric or multicentric disease. Unicentric disease is most often diagnosed by accident or by symptomatology resulting from compression upon the adjoining anatomical structures. Considering its lymphatic origin, tumor mass can theoretically occur in any body region. We present a case of paracardiac localization of
unicentric Castleman’s disease in a previously healthy 24-year-old woman. In such clinical cases, the specific localization of the tumor and its radiological properties can pose a differential diagnostic
dilemma. Correct diagnosis is only possible after complete surgical excision and histopathologic analysis, which is the optimal therapeutic approach in this disease.

Ključne riječi

Giant lymph node hyperplasia; Lymphatic vessels; Neoplasms; Rare diseases; Case reports

Hrčak ID:

161292

URI

https://hrcak.srce.hr/161292

Datum izdavanja:

1.3.2016.

Podaci na drugim jezicima: hrvatski

Posjeta: 2.196 *