Recenzija, prikaz
https://doi.org/10.20471/acc.2024.63.03-04.47
A Man with Uterine Leiomyoma as Part of Persistent Müllerian Duct Syndrome – a Case Report and Review of the Literature
Ivan Novak
; Ljudevit Jurak Department of Pathology and Cytology, Sestre milosrdnice University Hospital Center, Zagreb, Croatia
Igor Grubišić
; Department of Urology, Sestre milosrdnice University Hospital Center, Zagreb, Croatia
Ivan Pezelj
; Department of Urology, Sestre milosrdnice University Hospital Center, Zagreb, Croatia
Tihana Regović Džombeta
; Ljudevit Jurak Department of Pathology and Cytology, Sestre milosrdnice University Hospital Center, Zagreb, Croatia; Department of Pathology, School of Medicine, University of Zagreb, Zagreb, Croatia
Ivan Svaguša
; Department of Urology, Sestre milosrdnice University Hospital Center, Zagreb, Croatia
Goran Štimac
; Department of Urology, Sestre milosrdnice University Hospital Center, Zagreb, Croatia
Monika Ulamec
; Ljudevit Jurak Department of Pathology and Cytology, Sestre milosrdnice University Hospital Center, Zagreb, Croatia; Department of Pathology, School of Medicine, University of Zagreb, Zagreb, Croatia
*
Božo Krušlin
; Ljudevit Jurak Department of Pathology and Cytology, Sestre milosrdnice University Hospital Center, Zagreb, Croatia; Department of Pathology, School of Medicine, University of Zagreb, Zagreb, Croatia
* Dopisni autor.
Sažetak
We present a clinical case of a 59-year-old man, father of two children, who complained
of irritative voiding of the bladder. An unknown retrovesical structure was detected by ultrasound
and computed tomography, and was surgically removed later. Histopathologic analysis reported
uterine tissue with a leiomyoma, thus the diagnosis of persistent müllerian duct syndrome (PMDS)
was established. It is a rare disorder characterized by the appearance of müllerian derivatives (fallopian
tubes, uterus, and upper two-thirds of vagina) in males with normally developed external and internal
genitalia. Patients usually present with cryptorchidism and inguinal hernia. Irritative voiding has not
yet been described as the main symptom of PMDS. The major complications of the disorder are infertility,
testicular tumorigenesis, and malignant transformation of müllerian structures. To the best of our
knowledge, in addition to our case, only one case of PMDS with uterine leiomyoma has been described
in the literature so far.
Ključne riječi
Persistent müllerian duct syndrome; Leiomyoma; Uterus; Fertility; Lower urinary tract symptoms
Hrčak ID:
333371
URI
Datum izdavanja:
31.12.2024.
Posjeta: 749 *