Izvorni znanstveni članak
https://doi.org/10.20471/acc.2023.62.s3.2
Combined, novel management of bilateral varus hip deformity using "Eight-plate" in children with spondyloepiphyseal dysplasia congenita
Josip Vlaić
orcid.org/0000-0001-6381-8684
; Division of Paediatric Orthopaedic Surgery, Children’s Hospital Zagreb, Zagreb, Croatia; School of Medicine, University of Zagreb, Zagreb, Croatia
Tomislav Ribičić
; Division of Paediatric Orthopaedic Surgery, Children’s Hospital Zagreb, Zagreb, Croatia
Davor Bojić
; Division of Paediatric Orthopaedic Surgery, Children’s Hospital Zagreb, Zagreb, Croatia
Darko Antičević
orcid.org/0000-0001-6713-1273
; Josip Juraj Strossmayer University of Osijek, Faculty of dental medicine and health, Osijek, Croatia; Division of Orthopaedic Surgery, Specialty Hospital St. Catherine, Zagreb, Croatia
Sažetak
Spondyloepiphysal dysplasia congenita (SEDc) is a rare autosomal dominant genetic disorder. Femoral head ossification delay and the proximal femur varus deformity i.e. coxa vara (CV) are the major features of SEDc. The accepted treatment is a valgus femoral osteotomy. The data on hip surgery in SEDc are scarce. In our database from 2006 to 2020, there were 6 SEDc patients. Four patients had surgery on 8 hips. Surgical treatment was indicated due to progressive CV deformity i.e. a decreasing neck-shaft angle (NSA), pain, limited hip abduction, and gait disturbances. In three patients, a novel surgical treatment was applied – a greater trochanter apo-physiodesis using “Eight-plate”. The patients were evaluated clinically and radiologically. The median age at first surgery was 6.3 years (range, 3.2 to 9.5 y) and the median follow-up period was 7 years (range, 5.6 to 14 y). The postoperative NSA was significantly improved with a mean increase of 13 degrees (P<0.001). Additional surgeries were needed in two patients. Overall, our results showed improved clinical and radiological parameters. The purpose of this study was to determine whether a method using an “Eight- plate” applied early to greater trochanter apophysis in SEDc patients with bilateral CV could reduce the need for more aggressive surgery in near future.
Ključne riječi
Spondyloepiphysal dysplasia; hip; greater trochanter; surgery
Hrčak ID:
310003
URI
Datum izdavanja:
31.8.2023.
Posjeta: 247 *